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Vol. 29. Issue 7.
Pages 353-355 (October 1993)
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Vol. 29. Issue 7.
Pages 353-355 (October 1993)
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Fibromatosis agresiva. A propósito de un caso
Aggresive fibromatosis. One case
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J. Orón Alpuente*, M.A. González Jiménez, J. Ruiz del Castillo, J. Martínez-León, M.T. Chiquillo Barber, J.D. Orón Marqués
Departamento de Cirugía. Hospital Clínico Universitario. Valencia
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Se presenta un caso de fibromatosis agresiva infantil de localización en pared torácica. Esta afección de diagnóstico anato-mopatológico debe su nombre a su gran capacidad infiltrativa local y alta tasa de recidivas. Su aspecto clínico y radiológico hace sospechar en ocasiones que se trate de una tumoración maligna.

El tratamiento de elección consiste en la escisión amplia del tumor. Se revisan las nuevas opciones terapéuticas que se están ensayando por parte de varios autores como tratamiento adyuvante a la cirugía para evitar las recidivas.

One case of aggressive infantile fibromatosis of thoracic wall localization is presented. This anatomopathologic diagnostic involvement owes its name to the great local infiltrative capacity and high rate of recurrence. The clinical and radiologic appearance, may at times, lead malignant tumors to be suspected.

The treatment of choice consists in wide excision of the tumor. The new therapeutic options which are corrently being tried by several authors such as adjuvant therapy to surgery to avoid recurrence are reviewed.

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Bibliografía
[1.]
A.P. Stout.
Juvenile fibromatosis.
Cancer, 7 (1954), pp. 950-953
[2.]
R. López, N. Kemalyan, M.S. Moseley, D. Dennis, R.M. Vetto.
Problems in diagnosis and management of desmoid tumors.
Am J Surg, 159 (1989), pp. 450-453
[3.]
C. Baselga, A. Lario, M.J. López, B. Elboj, E. Bilbao, C. Pérez Castejón, J.L. Olivares, M. Bueno.
Hamartoma fibroso de pared costal. A propósito de un caso.
An Esp Pediatr, 20. 2 (1984), pp. 130-134
[4.]
D.H. Mackenzie.
The fibromatoses: A clinicopathological concept.
Br Med J, 4 (1972), pp. 227-281
[5.]
F.M. Enzinger, ShW. Weiss.
Fibromatoses. Soft tissue tumors.
Ed. Mosby, (1983), pp. 45-70
[6.]
F.M. Enzinger, M. Shiriak.
Musculoaponeurotic fibromatosis of the Shoulder Girdle.
Extraabdominal desmoid. Cancer, 20 (1967), pp. 1.131-1.140
[7.]
H.J. Griffiths, K. Robinson, T.A. Bonfiglio.
Aggressive fibromatosis.
Skel Rad, 9 (1983), pp. 179-184
[8.]
A.P. Stout, R. Latters.
Tumors of the soft tissue. Atlas of the tumor pathology. Two series. Fasc. one.
Armed Force Institute of Pathology, (1986), pp. 19-30
[9.]
P.J. McAdam.
Aggressive fibromatosis.
J Bone Joint Surg, 57–8 (1979), pp. 618-631
[10.]
J.J. Reitamo.
The desmoid tumor: choice of treatment, results and complications.
Arch Surg, 118 (1983), pp. 1.318-1.322
[11.]
J.J. Reitamo, T.M. Scheinin, P. Hayri.
The desmoid syndrome New aspects in the cause, pathogenesis and treatment of the desmoid tumor.
Am J Surg, 151 (1986), pp. 230-237
[12.]
D.W. Easter, N.A. Halasz.
Recent trends in the management of desmoid tumors. Summary of 19 cases and review of the literature.
Ann Surg, 210 (1989), pp. 765-769
[13.]
J. Pérez Payarols, J. Ilari Rocabert, J. Sánchez de Toledo, V. Martínez Ibáñez.
Fibromatosis agresiva. A propósito de 14 casos.
Rev Esp Pediatr, 41 (1985), pp. 13-17
[14.]
P. Hayri, J.J. Reitamo, S. Totterman, D. Hopfner-Hllikainen, A. Sivula.
The desmoid tumor: analysis of factors possibly contributing to the etiology and growth behavoir.
Am J Clin Pathol, 77 (1982), pp. 674-680
[15.]
G. Kalifa, G. Lalande, D. Larde, J. Bennet, C. Kalifa.
Les fibromes desmoides chez l’enfant.
Ann Radiol, 25 (1982), pp. 25-33
[16.]
M.C. Posner, M.H. Shiu, J.L. Newsome, S.I. Hajdu, J.J. Gaynor, M.F. Brennan.
The desmoid tumor: not a benign disease.
Arch Surg, 14 (1989), pp. 191-196
[17.]
P.W. Alien.
The fibromatoses: a clinicopathological classification bases on the 140 cases.
Am J Surg Path, 1 (1977), pp. 255-270
[18.]
A. Lanary, A. Lipschultz.
Effect of progesterone in desmoid tumor (aggressive fibromatosis).
N Engl J Med, 1.523 (1983), pp. 309-324
[19.]
L. Roggliv, H. Kim, E. Hawkins.
Congenital generalized fibromatosis with visceral involvement. A case report.
Cancer, 45 (1980), pp. 954-960
[20.]
J. Sánchez de Toledo, P. Plaja Román, J. Pérez Payareis, A. Fernández Teijeiro Álvarez, V. Martínez Ibáñez.
Medroxiprogesterona en el tratamiento de la fibromatosis agresiva.
Rev Esp Pediatr, 45 (1989), pp. 419-420
[21.]
W.R. Waddell, W.M. Kirsch.
Testolactone, Sulindac Warfarin and vitamin K1 for unresectable desmoid tumors.
Am J Surg, 161 (1991), pp. 416-420
[22.]
H. Rodríguez Cazar, M. Blanco del Moral.
Fibromatosis agresiva Fibroma desmoide extraabdominal.
Rev S And Traum y Ort, 5 (1985), pp. 225-232
[23.]
I.L. Atahan, F. Akyol, F. Zorlu, M. Gürkaynak.
Radiotherapy in the management of aggressive fibromatosis.
Br J Radiol, 62 (1989), pp. 854-856
[24.]
J.P. Bataina, C. Belloir, A. Mazabraud, et al.
Desmoid tumor in adults: the role of radiotherapy in their management.
Am J Surg, 155 (1988), pp. 754-760
Copyright © 1993. Sociedad Española de Neumología y Cirugía Torácica
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