Publique en esta revista
Información de la revista
Vol. 55. Núm. 7.
Páginas 378 (Julio 2019)
Compartir
Compartir
Descargar PDF
Más opciones de artículo
Vol. 55. Núm. 7.
Páginas 378 (Julio 2019)
Clinical Image
DOI: 10.1016/j.arbres.2018.10.013
Acceso a texto completo
Multiple Pulmonary and Hepatic Arteriovenous Malformations in a Patient With Rendu-Osler-Weber Disease
Malformaciones arteriovenosas pulmonares y hepáticas múltiples en un paciente con enfermedad de Rendu-Osler-Weber
Visitas
194
Emine Izgi, Fadime Guven, Hayri Ogul
Autor para correspondencia
drhogul@gmail.com

Corresponding author.
Department of Radiology, Faculty of Medicine, Ataturk University, Erzurum, Turkey
Información del artículo
Texto completo
Bibliografía
Descargar PDF
Estadísticas
Figuras (1)
Texto completo

A 63-year-old female presented with shortness of breath. Thoracoabdominal computed tomography (CT) angiography demonstrated multiple pulmonary and hepatic arteriovenous malformations (Fig. 1). Rendu-Osler-Weber disease is characterized by multiple mucocutaneous telangiectasias and visceral arteriovenous malformations.

Fig. 1.

Coronal MIP image (A) and anterior view volume rendering 3D (B) thoracoabdominal CT angiographies showing multiple pulmonary (arrows) and hepatic arteriovenous malformations (between brackets).

(0,22MB).

Osler-Weber-Rendu is an autosomal dominant disease. It is characterized by multiple mucocutaneous telangiectasias, recurrent epistaxis, and visceral arteriovenous malformations. Vascular structures of the lung and gastrointestinal tract frequently involve.1 With the advent of multidetector CT, hepatic and pulmonary involvement with Rendu-Osler-Weber is commonly recognized.1

In liver involvement of Rendu-Osler-Weber disease, there is shunting from the hepatic artery to the portal or hepatic veins.2 These vascular anastomoses can diagnosed by CT or catheter angiography. Transcatheter embolization of hepatic or pulmonary arteries can perform in lung or liver involvement of patients with Rendu-Osler-Weber disease. Transplantation can perform in patients with liver or pulmonary insufficiency.3

References
[1]
H. Ogul, Y. Aydın, M. Ozgokce, E. Orsal, M. Kantarci, A. Eroglu.
Pulmonary arteriovenous malformations and hepatic involvement in a patient with Osler-Rendu-Weber disease.
Ann Thorac Surg, 94 (2012), pp. e155
[2]
G. Garcia-Tsao, J.R. Korzenik, L. Young, K.J. Henderson, D. Jain, B. Byrd, et al.
Liver disease in patients with hereditary hemorrhagic telangiectasia.
N Engl J Med, 343 (2000), pp. 931-936
[3]
P. Lacombe, A. Lacout, P.Y. Marcy, S. Binsse, J. Sellier, M. Bensalah, et al.
Diagnosis and treatment of pulmonary arteriovenous malformations in hereditary hemorrhagic telangiectasia: an overview.
Diagn Interv Imaging, 94 (2013), pp. 835-848
Copyright © 2018. SEPAR
Idiomas
Archivos de Bronconeumología

Suscríbase a la newsletter

Opciones de artículo
Herramientas
es en

¿Es usted profesional sanitario apto para prescribir o dispensar medicamentos?

Are you a health professional able to prescribe or dispense drugs?

es en
Política de cookies Cookies policy
Utilizamos cookies propias y de terceros para mejorar nuestros servicios y mostrarle publicidad relacionada con sus preferencias mediante el análisis de sus hábitos de navegación. Si continua navegando, consideramos que acepta su uso. Puede cambiar la configuración u obtener más información aquí. To improve our services and products, we use "cookies" (own or third parties authorized) to show advertising related to client preferences through the analyses of navigation customer behavior. Continuing navigation will be considered as acceptance of this use. You can change the settings or obtain more information by clicking here.