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El síndrome de la cimitarra es una rara y compleja malformación habitualmente asintomática, cuyo diagnóstico se sospecha, en más del 50% de los casos, en la radiografía posteroanterior de tórax. El diagnóstico definitivo se obtiene mediante angiografía por sustracción digital (ASD), técnica mínimamente invasiva.
La corrección quirúrgica es requerida en pocos casos.
The Scimitar's syndrome is an uncommon and complex malformation often asymptomatic which diagnostic is suspected in the anteroposterior radiograph of the thorax in more than 50% of cases. The definitive diagnostic is obtained through angiography by digital subtraction (DSA), technique less invader.
The surgical correction is poorly required.
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Copyright © 1988. Sociedad Española de Neumología y Cirugía Torácica
