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Vol. 23. Issue 4.
Pages 196-199 (July - August 1987)
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Vol. 23. Issue 4.
Pages 196-199 (July - August 1987)
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Hemosiderosis pulmonar idiopatica. Dos casos en adultos
Idiopathic pulmonary hemosiderosis. Report of two adult patients with this disease
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J. Teran Santos, F. Zurbano Goñi, R. Agüero Balbin, L. Borderias Clau, J. Duran Cantolla, J.R. Sampedro Alvarez, R. Ondiviela
Servicio de Neumología. Hospital Nacional Marqués de Valdecilla. Santander
J. Vierna*
* Servicio de Anatomía Patológica. Hospital Nacional Marqués de Valdecilla. Santander
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La hemosiderosis pulmonar idiopática (HPI) es una enfermedad de etiología y patogenia desconocidas, caracterizada por episodios de hemorragias pulmonares de repetición, anemia ferropénica e insuficiencia respiratoria.

Presentamos dos casos de HPI en adultos, hombre y mujer, el primero vivo en la actualidad y la segunda que falleció tras seis años de seguimiento.

Se analizan el curso y características clínicas de la enfermedad, así como las diferentes técnicas etiopatogénicas y situación actual del tratamiento médico de esta enfermedad.

Idiopathic pulmonary hemosiderosis is a disease of unknown etiology and pathogenesis, and is characterized by recurrent pulmonary bleeding, iron defidency anaemia and respiratory failure.

We report on two adult patients, one male and one female. The former is still alive while the latter died after six years follow up. The outcome and clinical features of the disease, its etiopathogenic implications and the current status of its medical treatment are discussed.

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Copyright © 1987. Sociedad Española de Neumología y Cirugía Torácica
Archivos de Bronconeumología
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