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Vol. 42. Issue 10.
Pages 557-559 (October 2006)
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Vol. 42. Issue 10.
Pages 557-559 (October 2006)
Nota clínica
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Fibrosis pulmonar intersticial centrada en las vías aéreas asociada a inhalación de productos de limpieza
Airway-Centered Interstitial Fibrosis Related to Exposure to Fumes From Cleaning Products
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Mario Serranoa,
Corresponding author
buschito@yahoo.de

Correspondencia: Dr. M. Serrano. Servei de Pneumologia. Hospital Clínic. Villarroel, 170. 08036 Barcelona. España
, María Molina-Molinaa, José Ramírezb, Marcelo Sánchezc, Antoni Xaubeta
a Servei de Pneumologia. Hospital Clínic. Barcelona. España
b Servei de Anatomia Patològica. Hospital Clínic. Barcelona. España
c Servei de Radiodiagnòstic. Hospital Clínic. Barcelona. España
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La fibrosis pulmonar intersticial centrada en las vías aéreas es una entidad clinicopatológica poco conocida y de reciente descripción, que se caracteriza anatomopatológicamente por fibrosis bronquiolar y fibrosis pulmonar intersticial localizada alrededor de las vías aéreas. Esta enfermedad se ha relacionado con la inhalación de diversos agentes tanto ambientales como ocupacionales, de origen orgánico o inorgánico. Las manifestaciones clínicas, radiológicas y funcionales respiratorias son similares a las de las neumonías intersticiales idiopáticas.

Se describe un caso de fibrosis pulmonar intersticial centrada en las vías aéreas que fue secundaria a la inhalación de productos de limpieza.

Palabras clave:
Enfermedades pulmonares intersticiales difusas
Neumonías intersticiales idiopáticas
Fibrosis pulmonar intersticial centrada en las vías aéreas

Airway-centered interstitial fibrosis is a little known clinical entity that has only recently been described in the literature. Its pathology is characterized by bronchial fibrosis and localized interstitial pulmonary fibrosis around the airways. The disease has been associated with inhalation of a variety of substances, environmental or occupational, organic or inorganic. Clinical signs, radiographic manifestations, and lung function in patients with airway-centered interstitial fibrosis are similar to those of patients with idiopathic interstitial pneumonia.

We describe a case of airway-centered interstitial fibrosis related to exposure to fumes from cleaning products.

Key words:
Diffuse interstitial pulmonary disease
Idiopathic interstitial pneumonia
Airway-centered interstitial fibrosis
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Copyright © 2006. Sociedad Española de Neumología y Cirugía Torácica
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