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Vol. 35. Issue 5.
Pages 242-244 (May 1999)
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Vol. 35. Issue 5.
Pages 242-244 (May 1999)
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Síndrome de Kartagener. Diagnóstico en una paciente de 75 años
Kartagener's syndrome. Diagnosis in a 75-year-old woman
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F.J. Gómez de Terreros Caro1
Corresponding author
fjgtc@altavista.net

Correspondencia: Hilarión Eslava, 50, 4.ª dcha. 28015 Madrid.
, C. Gómez-Stern Aguilar, R. Álvarez-Sala Walther, C. Prados Sánchez, F. García Río, J. Villamor León
Servicio de Neumología. Hospital Universitario La Paz. Madrid
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El síndrome de Kartagener es una enfermedad hereditaria caracterizada por la tríada de bronquiectasias, sinusitis y situs inversus, motivada por un defecto ultraestructural de los cilios y que ocasiona una alteración del aclaramiento mucociliar. El diagnóstico se suele realizar en la infancia, pocos casos se diagnostican en la edad adulta y menos aún en mayores de 60 años. El tratamiento precoz y adecuado de las infecciones respiratorias puede evitar lesiones irreversibles en el pulmón. Se presenta el caso de una mujer con bronquiectasias, sinusitis y situs inversus, diagnosticada de síndrome de Kartagener mediante criterios clínicos a la edad de 75 años.

Palabras clave:
Síndrome de Kartagener
Discinesia ciliar primaria
Bronquiectasias
Geriatría

Kartagener's syndrome is an inherited disease characterized by the clinical triad of bronchiectasis, sinusitis and situs inversus caused by an ultrastructural defect in the cilia that results in impaired mucociliary clearance. It is usually diagnosed during childhood, with a small number of cases discovered in adults and even fewer among patients over 60 years of age. Prompt, appropriate treatment of respiratory infections can minimize irreversible lung damage. We report the case of a woman with bronchiectasis, sinusitis and situs inversus diagnosed of Kartagener's syndrome based on clinical signs at age 75 years.

Key words:
Kartagener's syndrome
Primary ciliary dyskinesia
Bronchiectasis and the elderly
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Copyright © 1999. Sociedad Española de Neumología y Cirugía Torácica
Archivos de Bronconeumología
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