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La linfangiomiomatosis es una proliferación aberrante de músculo liso atípico que afecta al sistema linfático y que se da exclusivamente en mujeres, generalmente en edad fértil. Se presenta un caso de una mujer de 32 años de edad con expectoración hemoptoica cuyo único hallazgo radiológico fue un patrón intersticial bilateral difuso. Se discuten sus características clínicas, radiológicas, funcionales y patológicas y se revisan las posibilidades terapéuticas.
Lymphangiomyomatosis is an aberrant proliferation of aty-pical smooth muscle which involves the lymphatic system and is exclusively found in témales, usually in fertile age. We report a 32-year-old female with bloodstained sputum in whom the only radiological finding was a diffuse bilateral interstitial pattern. The clinical, radiológica!, functional and pathological features are discussed, and the therapeutic possi-bilities are reviewed.
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