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Vol. 31. Issue 1.
Pages 37-39 (January 1995)
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Vol. 31. Issue 1.
Pages 37-39 (January 1995)
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Afectación intersticial pulmonar por hemocromatosis como forma de presentación de la enfermedad
Interstitial pulmonary involvement due to hemochromatosis as a presenting sign of disease
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M.E. Pereiro Alonso1, J.M. García García, M.A. Martínez Muñiz
Sección de Neumología. Hospital San Agustín. Avilés, Asturias
J.M. Alonso de la Campa*
* Servicio de Anatomía Patológica. Hospital San Agustín. Avilés, Asturias
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Presentamos un caso de hemocromatosis cuya primera manifestación fue el hallazgo casual de un patrón intersticial en la radiografía de tórax y en cuya biopsia transbronquial se demostró la presencia de hierro (Fe) en los macrófagos alveolares y material septal, lo que nos llevó a la búsqueda de depósitos en otras localizaciones, confirmándose su existencia en la biopsia hepática que mostró un Fe en peso seco de cilindro hepático (+): 6.964 μg.

Se ha revisado la literatura médica por el sistema CDROM Medline, año 1989 y hasta mayo de 1994, sin haber encontrado ninguna referencia al respecto.

Palabras clave:
Hemocromatosis
Patrón intersticial

We present a patient with hemochromatosis whose first sign of disease was an accidental finding of interstitial patterns on a chest film and whose transbronchial biopsy showed traces of iron (Fe) in alveolar macrophages and septal matter. We then looked for deposits in other locations, finding Fe ([+]: 6.964 μg) in the dry weight of a cylindrical sample of liver tissue.

A Medline search on CD-ROM for 1989 through May of 1994 revealed no references to similar cases.

Key words:
Hemochromatosis
Interstitial pattern
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Copyright © 1995. Sociedad Española de Neumología y Cirugía Torácica
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