Presentamos un caso clínico de un paciente joven, afectado de leiomiosarcoma pulmonar, diagnosticado en primera instancia como un quiste hidatídico. Para su diagnóstico definitivo fue necesario el estudio anatomopatológico de la pieza operatoria. Este raro tumor (menos de 100 casos en la literatura mundial) necesita diagnóstico diferencial con el carcinoma pulmonar ya que el leiomiosarcoma posee mejor pronóstico, siendo su tratamiento esencialmente quirúrgico.
We present the case of a young patient with leiomysarcoma of the lung that was at first diagnosed as a hydatid cyst. Pathological tissue analysis was needed for firm diagnosis. This rare tumor, of which fewer than 100 cases have been reported worldwide in the literature, needs to be considered as a differential diagnosis when lung cancer is suspected, given that leiomysarcoma has a better prognosis. Treatment is mainly surgical.
