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Vol. 37. Issue 11.
Pages 508-510 (November 2001)
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Vol. 37. Issue 11.
Pages 508-510 (November 2001)
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Aneurismas gigantes de la arteria pulmonar y trombosis venosa periférica (síndrome de Hughes-Stovin): regresión con tratamiento inmunosupresor
Giant aneurysms of the pulmonary artery and peripheral venous thrombosis (Hughes-Stovin syndrome): regression with immunosuppressant therapy
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A. Alí-Munivea,
Corresponding author
fnc@impsat.net.co
abrahamali_ali_munive@hotmail.com

Correspondencia: Dr. A. Ali-Munive. Fundación Neumológica Colombiana.Calle 163, A # 28–60. Bogotá, Colombia
, H. Varónb, D. Maldonadoa, C. Torres-Duquea
a Fundación Neumológica Colombiana
b Fundación Cardioinfantil. Instituto de Cardiología. Departamento de Radiología. Bogotá (Colombia)
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Presentamos el caso de un paciente joven de origen afro-caribeño, que consultó por tos seca y febrícula. En la radio-grafía del tórax de ingreso se observaron masas pulmonares hiliares bilaterales que, al ser evaluadas posteriormente con TC de tórax con contraste, se confirmó que correspondían a aneurismas gigantes de la arteria pulmonar. Su antecedente más importante era una trombosis venosa profunda detecta-da 6 meses antes de su ingreso. Se estableció el diagnóstico de síndrome de Hughes-Stovin y se inició tratamiento con prednisolona y azatioprina. La TC realizada 6 meses des-pués de tratamiento ininterrumpido demostró la desapari-ción de los aneurismas

El síndrome de Hughes-Stovin se caracteriza por aneuris-mas de las arterias pulmonares y trombosis venosa profun-da periférica. Puede cursar con complicaciones pulmonares graves, como hemoptisis y trombosis dentro de los aneuris-mas. Se ha considerado una variedad de la enfermedad de Behçet

Palabras clave:
Síndrome de Hughes-Stovin
Aneurismas de ar-terias pulmonares
Enfermedad de Behçet

We report the case of a young Afro-Caribbean patient who complained of dry cough and low-grade fever. A chest film upon admission showed bilateral hilar masses in the lungs, which a CT scan with contrast medium confirmed were giant aneurysms of the pulmonary artery. The most relevant past history was deep venous thrombosis six months before admission. Hughes-Stovin syndrome was diagnosed and tre-atment was started with prednisolone and azathioprine. A scan 6 months after treatment ended showed the aneurysms had disappeared. Hughes-Stovin syndrome is characterized by pulmonary artery aneurysms and peripheral deep ve-nous thromboses. Severe lung complications can include he-moptysis and thromboses inside the aneurysms. Hughes-Stovin syndrome has been considered a variety of Behçet's disease

Keywords:
Hughes-Stovin syndrome
Pulmonary arter aneurysms
Behçet's disease
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Bibliografía
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Copyright © 2001. Sociedad Española de Neumología y Cirugía Torácica
Archivos de Bronconeumología
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